Infantile malignant peripheral nerve sheath tumour of the ileum causing ileo-ileal intussusception in an infant.

Nerve sheath tumours are rare tumours. We report here for the first time a malignant peripheral nerve sheath tumour of the ileum in a child who presented with recurrent intussusceptions. The tumour was excised with wide margins and staging procedures did not show any metastatically suspicious lesions. Complete resection in non-metastatic tumours seems to be the therapy of choice.