Tabuchi Keiji, Okubo Hideki, Takahashi Kazuhiko, Uemaetomari Isao, Shimoyamada Hiroaki, Nakayama Yoshio, Hara Akira
Department of Otolaryngology, Institute of Clinical Medicine, University of Tsukuba, 1-1-1 Tennodai, 305-8575, Tsukuba, Japan.
Auris Nasus Larynx. 2003 Dec;30(4):421-3. doi: 10.1016/s0385-8146(03)00092-0.
Nevoid basal cell carcinoma syndrome, also referred to as Gorlin-Goltz syndrome, is a rare autosomal dominant disorder characterized by multiple basal cell carcinomas, jaw cysts, palmar or plantar pits, ectopic calcification of the falx cerebri, and various skeletal developmental abnormalities. A minority of basal cell carcinomas demonstrate aggressive behavior and involve the craniofacial bones in nevoid basal cell carcinoma syndrome. A non-familial case of nevoid basal cell carcinoma syndrome with a basal cell carcinoma of the eyelid invading to the ethmoid sinus is reported.
痣样基底细胞癌综合征,也称为戈林-戈尔茨综合征,是一种罕见的常染色体显性疾病,其特征为多发性基底细胞癌、颌骨囊肿、掌跖凹、大脑镰异位钙化以及各种骨骼发育异常。少数基底细胞癌表现出侵袭性,在痣样基底细胞癌综合征中累及颅面骨。本文报道了1例非家族性痣样基底细胞癌综合征病例,其眼睑基底细胞癌侵犯至筛窦。