Quinones-Hinojosa Alfredo, Gadkary Chirag A, Mummaneni Praveen V, Rosenberg William S
Department of Neurological Surgery, University of California, San Francisco, San Francisco, California 94143, USA.
Surg Neurol. 2004 Feb;61(2):201-3; discussion 203. doi: 10.1016/s0090-3019(03)00431-2.
Split spinal cord malformations (SCM) typically present in childhood and rarely in adulthood. Very little is known about the SCMs in the elderly, and the diagnosis can be easily missed. A 73-year-old woman with a childhood history of scoliosis and late ambulation milestones presented with a 2-year history of worsening low back pain and progressive difficulty walking. She had a mild gait disturbance with 4/5 weakness in left ankle dorsiflexion. Magnetic resonance imaging revealed a bifid spinal cord contained in a single thecal sac and a tethered cord with low-lying conus at L3. The patient was taken to the operating room and a soft-tissue median septum, as well as all other adhesions, was removed. The filum terminale was identified, coagulated, and divided. Six weeks later, the patient reported decreased back pain, improvement in ambulation, and markedly decreased used of narcotics for her back and leg pain. Her left ankle dorsiflexion strength improved to 4+/5. This patient had two hemicords encased in a single dural tube separated by a nonrigid, fibrous median septum and an associated tethered cord. Adult presentation of SCM is extremely rare. This case highlights the need to consider split cord malformation and tethered cord in the differential diagnosis not only for adults but also the elderly presenting with back pain, scoliosis, and difficulty walking.
脊髓纵裂畸形(SCM)通常在儿童期出现,成年期很少见。关于老年人的脊髓纵裂畸形知之甚少,诊断很容易被遗漏。一名73岁女性,有儿童期脊柱侧弯病史且学步里程碑延迟,出现了2年的下背部疼痛加重和进行性行走困难。她有轻度步态障碍,左踝背屈肌力为4/5。磁共振成像显示,单个硬膜囊内有一个双裂脊髓以及脊髓栓系伴L3水平低位圆锥。患者被送往手术室,切除了软组织正中隔以及所有其他粘连。识别、凝固并切断终丝。六周后,患者报告背痛减轻、行走改善,用于背部和腿痛的麻醉药用量明显减少。她的左踝背屈肌力提高到4+/5。该患者有两根半脊髓被包裹在一个单一的硬脊膜管内,由一个非刚性的纤维性正中隔分隔开,并伴有脊髓栓系。脊髓纵裂畸形在成人中极为罕见。该病例强调,在鉴别诊断中不仅要考虑成人,也要考虑出现背痛、脊柱侧弯和行走困难的老年人的脊髓纵裂畸形和脊髓栓系。