Cervantes Bustamante Roberto, Ocampo del Prado Luis Carlos, Zárate Mondragón Flora, Mata Rivera Norberto, Ramírez-Mayans Jaime A, Mora Tiscareño María Antonieta, García Campos L N
Servicio de Gastroenterología y Nutrición Pediátrica, Instituto Nacional de Pediatría (INP), Insurgentes Sur 3700-C, Col. Insurgentes Cuicuilco, 04530 México, D.F. Correo.
Rev Gastroenterol Mex. 2003 Oct-Dec;68(4):266-70.
Peutz-Jeghers syndrome is an autonomic dominant disease characterized by hamartomatous polyps and mucocutaneous hyperpigmentation. We present 16 cases; females were more affected. The most common presenting complaints were of gastrointestinal tract. All polyps found were hamartomatous with general distribution through gastrointestinal tract. Endoscopic polypectomy should be carried out for treatment. Radiologic, endoscopic and histologic studies should be conducted for long-term follow-up, because of high risk of malignancy.
佩-吉综合征是一种常染色体显性疾病，其特征为错构瘤性息肉和黏膜皮肤色素沉着。我们报告了16例病例，女性受影响更多。最常见的主诉是胃肠道问题。所有发现的息肉均为错构瘤性，广泛分布于胃肠道。治疗应进行内镜下息肉切除术。由于恶性风险高，应进行放射学、内镜和组织学研究以进行长期随访。
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