Refsum Helga, Fredriksen Ase, Meyer Klaus, Ueland Per M, Kase Bengt Frode
Department of Pharmacology, University of Oxford, United Kingdom.
J Pediatr. 2004 Jun;144(6):830-2. doi: 10.1016/j.jpeds.2004.03.004.
Serious complications of homocystinuria caused by cystathionine beta-synthase deficiency can be prevented by early intervention. We determined the prevalence of 6 specific mutations in 1133 newborn blood samples. Our results suggest that homocystinuria is more common than previously reported. Newborn screening for homocystinuria through mutation detection should be further considered.
由胱硫醚β-合酶缺乏引起的同型胱氨酸尿症的严重并发症可通过早期干预预防。我们测定了1133份新生儿血样中6种特定突变的发生率。我们的结果表明,同型胱氨酸尿症比之前报道的更为常见。应进一步考虑通过突变检测对同型胱氨酸尿症进行新生儿筛查。