Xu Luting, Olivry Thierry, Chan Lawrence S
Department of Dermatology, North-western University Medical School, Chicago, IL, USA.
Vet Dermatol. 2004 Jun;15(3):146-51. doi: 10.1111/j.1365-3164.2004.00373.x.
Bullous pemphigoid is an autoimmune blistering human skin disease mediated by immunoglobulin (Ig)G autoantibodies targeting skin basement membrane component type XVII collagen, a transmembrane protein. Also designated BP180 and BPAG2, type XVII collagen is an extracellular matrix element essential for the connection between the epidermis and the underlying dermis. In addition to being a target antigen in the human disease bullous pemphigoid, type XVII collagen is also targeted by autoantibodies of canine, feline, equine and porcine patients suffering from a similar blistering skin disease. Previously, enzyme-linked immunosorbent assay and Western blot analyses have shown that autoantibodies from pigs affected with bullous pemphigoid recognize the human NC16A domain of type XVII collagen. To facilitate the development of porcine model of bullous pemphigoid, we isolated cDNA encoding the porcine type XVII collagen NC16A domain using a reverse transcription-polymerase chain reaction technique. The amino acids deduced from the NC16A cDNA showed 61% identity with the sequence of human NC16A. An antibody generated against a 20-amino acid peptide within the porcine NC16A localized the NC16A epitope to the upper part of porcine skin basement membrane zone. Our data provide further information of the porcine bullous pemphigoid target antigen and may help investigators for their further studies of this disease.
大疱性类天疱疮是一种自身免疫性水疱性人类皮肤病,由针对皮肤基底膜成分XVII型胶原蛋白(一种跨膜蛋白)的免疫球蛋白(Ig)G自身抗体介导。XVII型胶原蛋白也被称为BP180和BPAG2,是表皮与下方真皮之间连接所必需的细胞外基质成分。除了是人类疾病大疱性类天疱疮的靶抗原外,XVII型胶原蛋白也是患有类似水疱性皮肤病的犬、猫、马和猪患者自身抗体的靶标。此前,酶联免疫吸附测定和蛋白质印迹分析表明,患有大疱性类天疱疮的猪的自身抗体可识别XVII型胶原蛋白的人NC16A结构域。为了促进大疱性类天疱疮猪模型的开发,我们使用逆转录-聚合酶链反应技术分离了编码猪XVII型胶原蛋白NC16A结构域的cDNA。从NC16A cDNA推导的氨基酸与人NC16A序列显示出61%的同一性。针对猪NC16A内一个20个氨基酸的肽产生的抗体将NC16A表位定位到猪皮肤基底膜带的上部。我们的数据提供了猪大疱性类天疱疮靶抗原的更多信息,并可能有助于研究人员对该疾病的进一步研究。