一名患有遗传性出血性毛细血管扩张症（奥斯勒氏病）的患者进行二次二尖瓣置换术。

A second mitral valve replacement in a patient with hereditary hemorrhagic telangiectasia (Osler's disease).

作者信息

Ishikawa Susumu, Oshima Kiyohiro, Aizaki Masahiro, Takahashi Toru, Hasegawa Yutaka, Morishita Yasuo

机构信息

Second Department of Surgery, Gunma University Faculty of Medicine, Gunma 371-8511, Japan.

出版信息

Jpn Heart J. 2004 Sep;45(5):885-8. doi: 10.1536/jhj.45.885.

DOI:10.1536/jhj.45.885

PMID:15557731

Abstract

A 62-year-old female with Osler's disease was admitted to our hospital because of fever and cardiac failure. The patient had undergone a mitral valve replacement (MVR) using a Carpentier-Edwards prosthetic valve 14 years earlier. A bacterial examination of arterial blood identified Streptococcus mitis. No arteriovenous malformations were detected in visceral organs. The patient underwent MVR using the same prosthetic xenograft after conservative treatment and management of repetitive epistaxis and decayed teeth. Intra- and postoperative bleeding were typical of a mitral valve reoperation. This is the first reported experience, to the best of our knowledge, of a second MVR in a patient with Osler's disease.

摘要

一名患有奥斯勒病的62岁女性因发热和心力衰竭入住我院。该患者14年前曾使用卡彭蒂埃-爱德华兹人工瓣膜进行二尖瓣置换术（MVR）。动脉血细菌检查发现缓症链球菌。在内脏器官中未检测到动静脉畸形。在对反复鼻出血和龋齿进行保守治疗和处理后，患者使用相同的人工异种移植物进行了MVR。术中和术后出血是二尖瓣再次手术的典型情况。据我们所知，这是首例关于奥斯勒病患者进行第二次MVR的报道。