Kameyama A, Sato Y, Ishizu T, Takano T, Saito T
Department of Internal Medicine, Ibara City Hospital.
Kokyu To Junkan. 1992 Apr;40(4):397-401.
The presence of myocardial involvement is rare in benign Duchenne type of progressive muscular dystrophy (Becker's muscular dystrophy). We describe two brothers suffering from Becker's muscular dystrophy, both of whom presented with dilated cardiomyopathy. The first case is a 39-year-old male who had suffered from gait disturbance from the age of 17. When 37 years old, he was found to have heart disease. When he first came to our hospital, pseudohypertrophy of the calves was present. Chest radiography, electrocardiogram, ultrasonocardiography and clinical feature indicated Becker's muscular dystrophy with dilated cardiomyopathy. The second case is the younger brother of the 37-year old male. He suffered from leg weakness. He came to our hospital with the chief complaint of discomfort of the anterior chest. Pseudohypertrophy of the calves was present. Chest radiography, electrocardiogram, ultrasonogram indicated dilated cardiomyopathy.
在良性杜氏型进行性肌营养不良(贝克型肌营养不良)中,心肌受累的情况较为罕见。我们描述了两名患有贝克型肌营养不良的兄弟,他们都出现了扩张型心肌病。首例患者为一名39岁男性,自17岁起就患有步态障碍。37岁时,他被发现患有心脏病。初次来我院就诊时,其小腿存在假性肥大。胸部X线、心电图、超声心动图及临床特征均表明为贝克型肌营养不良合并扩张型心肌病。第二例是该37岁男性的弟弟。他有腿部无力症状。因前胸不适为主诉前来我院就诊。小腿存在假性肥大。胸部X线、心电图、超声检查均显示为扩张型心肌病。