巨大型颅骨硬膜外原发性纤维黄色瘤：一例报告

Giant cranial extradural primary fibroxanthoma: a case report.

作者信息

Usul Haydar, Kuzeyli Kayhan, Cakir Ertuğrul, Caylan Refik, Sayin Ozgür C, Peksoylu Bekircan, Karaarslan Gökalp

机构信息

Department of Neurosurgery, Karadeniz Technical University School of Medicine, Trabzon TR-61080, Turkey.

出版信息

Surg Neurol. 2005 Mar;63(3):281-4. doi: 10.1016/j.surneu.2004.02.036.

DOI:10.1016/j.surneu.2004.02.036

PMID:15734528

Abstract

Primary fibroxanthoma of the cranium is an extremely rare condition. Xanthomatous tumors of the central nervous system are occasionally associated with diseases such as Hand-Schuler-Christian disease, malignant fibrous histiocytoma, hyperlipidemia, and a complication of metabolic or storage disorders. However, until 2003, only a few cases of primary fibroxanthoma have been reported. We report a giant fibroxanthoma destroying the lateral skull base unaccompanied by a systemic or metabolic disease.

摘要

颅骨原发性纤维黄色瘤是一种极为罕见的病症。中枢神经系统的黄色瘤性肿瘤偶尔与诸如汉-许-克病、恶性纤维组织细胞瘤、高脂血症以及代谢或贮积障碍的并发症等疾病相关。然而，直至2003年，仅报道过少数几例原发性纤维黄色瘤。我们报告一例巨大纤维黄色瘤，其破坏外侧颅底，且无全身性或代谢性疾病。