经颈静脉肝内门体分流术治疗布加综合征

Transjugular intrahepatic cavoportal shunt for Budd-Chiari syndrome.

作者信息

Ul Haq T, Munir K, Haider Z, Yaqoob J, Usman U

机构信息

Department of Radiology, The Aga Khan University Hospital, Karachi, Pakistan.

出版信息

Australas Radiol. 2005 Apr;49(2):140-3. doi: 10.1111/j.1440-1673.2005.01358.x.

DOI:10.1111/j.1440-1673.2005.01358.x

PMID:15845052

Abstract

Budd-Chiari syndrome (BCS) is characterized by obstruction of the hepatic venous outflow tract. Therapeutic options for BCS are limited. We report a case of a 21-year-old woman with protein S and C deficiency with gross ascites. Treatment with transjugular intrahepatic portosystemic shunt (TIPS) was attempted, which revealed occluded hepatic veins, so transcaval TIPS was performed. No serious procedure-related complication occurred. After successful shunt creation, the patient's symptoms subsided and she was discharged and followed up for 6 months.

摘要

布加综合征（BCS）的特征是肝静脉流出道梗阻。BCS的治疗选择有限。我们报告一例21岁患有蛋白S和C缺乏症且有大量腹水的女性病例。尝试行经颈静脉肝内门体分流术（TIPS）治疗，结果显示肝静脉闭塞，因此实施了经腔TIPS。未发生严重的与手术相关的并发症。成功建立分流后，患者症状缓解，出院并随访6个月。