Halioui-Louhaichi S, Azzabi O, Nefzi L, Ben Hariz M, Ben Mrad N, Ben Ammar B, Maherzi A
Service de pédiatrie, hôpital Mongi-Slim, La-Marsa, Tunisie.
Arch Pediatr. 2005 Jul;12(7):1120-3. doi: 10.1016/j.arcped.2005.03.044.
Cushing's syndrome reveals McCune-Albright syndrome in a minority of patients. Bilateral adrenalectomy is performed on the majority of cases.
We present a case of McCune-Albright syndrome revealed by a Cushing's syndrome treated by metyrapone. Results were good, after a 4-year follow up.
Treatment with metyrapone could be recommended, for some patients, in McCune-Albright syndrome with Cushing's syndrome before chirurgical treatment.
少数库欣综合征患者患有McCune-Albright综合征。大多数病例会进行双侧肾上腺切除术。
我们报告一例因库欣综合征而被发现的McCune-Albright综合征病例,该病例采用甲吡酮进行治疗。经过4年的随访,结果良好。
对于一些患有库欣综合征的McCune-Albright综合征患者,在手术治疗前,可推荐使用甲吡酮进行治疗。