Romero Frederico Ramalho, Fucs Moacyr, Castro Marília Germanos de, Garcia Carlos Ricardo Camargo, Fernandes Roni de Carvalho, Perez Marjo Deninson Cardenuto
Department of Urology, Santa Casa Medical School, Sao Paulo, Brazil.
Urology. 2005 Jul;66(1):194-5. doi: 10.1016/j.urology.2005.01.024.
Persistent müllerian duct syndrome is an unusual disorder characterized by cryptorchidism and retention of müllerian derivatives (uterus, fallopian tubes, and upper vagina). We report the case of a 39-year-old man with this syndrome in association with adenocarcinoma from the retained müllerian remnants of probable endocervical origin. To our knowledge, this is the first report of an endocervical adenocarcinoma associated with persistent müllerian duct syndrome.
持续性苗勒管综合征是一种罕见的疾病，其特征为隐睾症和苗勒管衍生物（子宫、输卵管和阴道上段）的残留。我们报告一例39岁患有此综合征的男性病例，其合并有源自可能的宫颈内膜的残留苗勒管组织的腺癌。据我们所知，这是首例与持续性苗勒管综合征相关的宫颈内膜腺癌的报告。
