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Klippel-Trenaunay syndrome with small vessel pulmonary arterial hypertension.
Thorax. 2005 Nov;60(11):971-3. doi: 10.1136/thx.2004.023184.
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[Rare cause of chronic recurrent pulmonary emboli and pulmonary artery hypertension].
Dtsch Med Wochenschr. 2006 Apr 13;131(15):811-4. doi: 10.1055/s-2006-939851.
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Klippel-Trenaunay-Weber syndrome with recurrent pulmonary embolism.
Clin Nucl Med. 1991 Apr;16(4):253-5. doi: 10.1097/00003072-199104000-00010.
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Klippel-Trenaunay-Weber syndrome as a cause of chronic thromboembolic pulmonary hypertension.
BMJ Case Rep. 2018 Mar 22;2018:bcr-2018-224621. doi: 10.1136/bcr-2018-224621.
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Vascular malformations as underlying cause of chronic thromboembolism and pulmonary hypertension.
J Plast Reconstr Aesthet Surg. 2009 May;62(5):684-9; discussion 689. doi: 10.1016/j.bjps.2007.12.062. Epub 2008 Jun 19.
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Pulmonary thromboendarterectomy in Klippel-Trénaunay syndrome.
J Thorac Cardiovasc Surg. 2010 Sep;140(3):e41-3. doi: 10.1016/j.jtcvs.2010.03.030.
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Klippel-Trenaunay syndrome as a rare cause of chronic thromboemboembolic pulmonary hypertension.
Respir Med Res. 2019 Nov;76:48-53. doi: 10.1016/j.resmer.2019.06.002. Epub 2019 Jul 9.
9
Chronic pulmonary embolism in Klippel-Trenaunay syndrome.
J Am Acad Dermatol. 2012 Jan;66(1):71-7. doi: 10.1016/j.jaad.2010.12.002. Epub 2011 May 14.
10
Pulmonary thromboembolism associated with Klippel-Trenaunay syndrome.
Pediatrics. 2005 Oct;116(4):e596-600. doi: 10.1542/peds.2004-1607. Epub 2005 Sep 15.

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Characterization of thrombosis in patients with Proteus syndrome.
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