Thölke Adina, Feller Gabriele, Schadendorf Dirk, Goerdt Sergij
Klinik für Dermatologie, Venerologie und Allergologie am Klinikum Mannheim gGmbH, Universitätsklinikum der Ruprecht-Karls-Universität Heidelberg.
J Dtsch Dermatol Ges. 2004 May;2(5):357-9.
Pityriasis rubra pilaris (PRP) is a rare idiopathic erythematosquamous disorder. Griffiths proposed five clinical and prognostic forms: (1) classic adult, (2) atypical adult, (3) classic juvenile, (4) circumscribed juvenile and (5) atypical juvenile. A 2 1/2 year old boy presented with type 3 PRP; as is typical, the skin eruption was preceded by an infectious disorder. Although type 3 PRP normally shows spontaneous resolution after several months to years, our young patient had a severe and protracted course, only responding to systemic retinoids.
红皮病型毛发红糠疹(PRP)是一种罕见的特发性红斑鳞屑性疾病。格里菲思提出了五种临床和预后类型:(1)经典成人型,(2)非典型成人型,(3)经典青少年型,(4)局限性青少年型和(5)非典型青少年型。一名2岁半的男孩患3型PRP;通常情况下,皮疹出现前有感染性疾病。虽然3型PRP通常在数月至数年后会自发消退,但我们这位年轻患者病情严重且病程迁延,仅对系统性维甲酸有反应。