Dagher Ibrahim, Franco Dominique
Service de Chirurgie, Hôpital Antoine-Béclère, Clamart.
Gastroenterol Clin Biol. 2005 Aug-Sep;29(8-9):875-7. doi: 10.1016/s0399-8320(05)86363-8.
The role of surgery in cystic diseases of the liver and biliary tract depends upon the kind of cysts. When they are symptomatic, solitary cysts of the liver may require laparoscopic unroofing. Mucinous cystadenoma should be resected since there is a risk of cystadenocarcinoma. Polycystic liver disease may require surgery when massive hepatomegaly results in pain or a worsening of the patient's general condition. Laparoscopic fenestration and partial hepatectomy are only indicated in a small number of selected patients with large or localized cysts. Orthotopic liver transplantation may be recommended in symptomatic cases with massive hepatomegaly even if there is no renal failure and no need for renal transplantation. Caroli's syndrome localized in one lobe or one segment should be resected since it leads to cholangiocarcinoma in more than 10% of cases. When cystic dilatations are diffuse, liver transplantation may be required. Choledochal cysts should be completely resected since cancer may arise in non resected parts. Complete resection may be associated with major hepatectomy.
手术在肝脏和胆道囊性疾病中的作用取决于囊肿的类型。当肝孤立性囊肿出现症状时,可能需要进行腹腔镜去顶术。黏液性囊腺瘤应予以切除,因为存在囊腺癌的风险。多囊肝疾病在出现巨大肝肿大导致疼痛或患者一般状况恶化时可能需要手术治疗。腹腔镜开窗术和部分肝切除术仅适用于少数选定的有大囊肿或局限性囊肿的患者。对于有症状且肝肿大明显的病例,即使没有肾衰竭且无需肾移植,也可能建议进行原位肝移植。局限于一个叶或一个节段的卡罗里综合征应予以切除,因为在超过10%的病例中会导致胆管癌。当囊性扩张弥漫时,可能需要进行肝移植。胆总管囊肿应完全切除,因为未切除部分可能发生癌变。完全切除可能需要进行大范围肝切除术。