Sarukawa Shunji, Sugawara Yasushi, Park Susam
Department of Plastic and Reconstructive Surgery, University of Tokyo, Tokyo, Japan.
J Craniofac Surg. 2006 Jan;17(1):147-51; discussion 151-2. doi: 10.1097/01.scs.0000193551.94175.9f.
Patients with Apert syndrome show hypertelorism and midfacial hypoplasia, and their features are significantly improved through facial bipartition surgery. In addition, because patients with Apert syndrome demonstrate cranial deformity as well as other deformities, they require multiple surgical interventions throughout their development. We present herein a girl with Apert syndrome for whom subcranial facial bipartition was performed. We could not use the coronal approach because she had a terribly cicatricial scalp and wide calvarial defects caused by previous cranial surgeries carried out at another institution. Therefore, we used the glabellar reverse V-shaped approach and temporal approaches in place of the standard approach. She enjoyed a complication-free intraoperative and postoperative course, and left the hospital on postoperative day 10. Her midfacial segment was repositioned 6 mm anteriorly and 12 mm inferiorly on the cephalometric measurement. Her interpupillary distance was altered from 83 mm preoperatively to 76 mm postoperatively. The reverse V-shaped glabellar approach permits more relaxation of the nasal skin and nasal augmentation that is more reliable, although an inconspicuous scar remains in the prominent area. The temporal approach is also useful, enabling easy zygomatic arch osteotomy and secure pterygo-maxillary separation for pterygo-maxillary separation through an oral approach, allowing chiseling toward the skull base.
患有Apert综合征的患者表现为眼距过宽和面部中部发育不全,通过面部二分法手术,他们的容貌有显著改善。此外,由于患有Apert综合征的患者除了其他畸形外还表现出颅骨畸形,因此他们在整个发育过程中需要多次手术干预。我们在此介绍一位接受了颅下面部二分法手术的Apert综合征女孩。我们不能采用冠状入路,因为她有严重的瘢痕性头皮以及由另一家机构先前进行的颅骨手术导致的广泛颅骨缺损。因此,我们采用眉间倒V形入路和颞部入路替代标准入路。她术中和术后过程均无并发症,术后第10天出院。根据头影测量,她的面部中段向前移位6毫米,向下移位12毫米。她的瞳孔间距从术前的83毫米变为术后的76毫米。眉间倒V形入路能使鼻皮肤有更多松弛,鼻隆突更可靠,尽管在突出区域会留下不明显的瘢痕。颞部入路也很有用,可以轻松进行颧弓截骨,并通过口腔入路安全地进行翼突 - 上颌分离,便于向颅底凿骨。