Uslu Nevzat, Gorgulu Sevket, Yildirim Aydin, Eren Mehmet
Siyami Ersek Thoracic and Cardiovascular Surgery Center, Department of Cardiology, Istanbul, Turkey.
Cardiology. 2006;105(3):155-7. doi: 10.1159/000091290. Epub 2006 Feb 7.
Accessory mitral valve tissue is a rare anomaly of embryologic development of the endocardial cushion and may cause substantial and progressive obstruction of the left ventricular outflow tract. Subaortic obstruction resulting from accessory mitral tissue is most likely due to systolic ballooning of the tissue into the outflow tract. The obstruction can occur in the early period of life as a result of mass effect or it can develop gradually due to the continued deposition of fibrous tissues within the left ventricular outflow tract. In patients with accessory mitral valve tissue, surgery is mandatory if there is a significant obstruction in the left ventricular outflow tract. We report two cases with accessory mitral valve tissue causing mild subaortic stenoses which did not require surgery.
二尖瓣附属组织是心内膜垫胚胎发育的一种罕见异常,可能导致左心室流出道严重且进行性梗阻。二尖瓣附属组织导致的主动脉瓣下梗阻最可能是由于该组织在收缩期膨出至流出道所致。梗阻可因肿块效应在生命早期出现,也可因左心室流出道内纤维组织的持续沉积而逐渐发展。对于有二尖瓣附属组织的患者,如果左心室流出道存在明显梗阻,则必须进行手术。我们报告两例二尖瓣附属组织导致轻度主动脉瓣下狭窄且无需手术的病例。