西地那非治疗肺动脉单侧发育不全继发的肺动脉高压
Sildenafil in pulmonary hypertension secondary to unilateral agenesis of pulmonary artery.
作者信息
Hamdan M A, Abu-Sulaiman R M, Najm H K
机构信息
Section of Pediatric Cardiology, King Abdulaziz Cardiac Center, King Fahad National Guard Hospital, Riyadh, Saudi Arabia.
出版信息
Pediatr Cardiol. 2006 Mar-Apr;27(2):279-81. doi: 10.1007/s00246-005-1100-7.
Unilateral agenesis of the pulmonary artery (PA) is a rare anomaly that can lead to pulmonary hypertension (PHTN). We report the case of a 10-month-old female with agenesis of the left PA, ventricular septal defect, and patent ductus arteriosus who developed PHTN precluding surgical repair. The use of sildenafil decreased PA pressure and normalized pulmonary vascular resistance, after which surgery was successfully performed.
单侧肺动脉发育不全是一种可导致肺动脉高压（PHTN）的罕见畸形。我们报告了一例10个月大的女性病例，其患有左肺动脉发育不全、室间隔缺损和动脉导管未闭，并发肺动脉高压，无法进行手术修复。使用西地那非后，肺动脉压力降低，肺血管阻力恢复正常，随后成功进行了手术。
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