Mimura Shinichiro, Kikura Mutsuhito, Itagaki Taiga, Inokuma Mie, Iwamoto Tatsuaki, Kawakubo Atsushi, Hirano Kazuhiro, Sato Shigehito
Department of Anesthesiology, Hamamatsu Medical Center, Hamamatsu 432-8580.
Masui. 2006 Apr;55(4):471-4.
Tuberous sclerosis (Bourneville-Pringle disease) is a rare disease with a triad of mental retardation, epilepsy, and facial spot. Management of the patients with tuberous sclerosis under general anesthesia has been previously reported. However, there are few case reports about management under general anesthesia of a pediatric patient with tuberous sclerosis with frequent epileptic seizure. Here, we report a case of a pediatric patient with tuberous sclerosis and frequent epileptic seizure who underwent intensive dental treatment under general anesthesia with careful management of epilepsy. The patient was discharged on the day of surgery without any complications. In this case report, we discussed the appropriate assessment of the complications of tuberous sclerosis; such as, of central nervous, circulatory, respiratory, endocrine, and urinary systems including the management of general anesthesia.
结节性硬化症(布尔内维尔-普林格尔病)是一种罕见疾病,具有智力发育迟缓、癫痫和面部斑疹三联征。先前已有关于结节性硬化症患者全身麻醉管理的报道。然而,关于频繁癫痫发作的结节性硬化症儿科患者全身麻醉管理的病例报告却很少。在此,我们报告一例结节性硬化症且频繁癫痫发作的儿科患者,在全身麻醉下接受强化牙科治疗,并对癫痫进行了精心管理。患者在手术当天出院,无任何并发症。在本病例报告中,我们讨论了对结节性硬化症并发症的适当评估,如中枢神经、循环、呼吸、内分泌和泌尿系统的并发症,包括全身麻醉的管理。