Refass Afaf, Bozorg Grayeli Alexis, Bouccara Didier, Ismail Mustapha, Cyna-Gorse Francoise, Cazals-Hatem Dominique, Sterkers Olivier
Otolaryngology Department, Hôpital Beaujon, AP-HP, 100 Boulevard du Général Leclerc, 92118, Clichy, France.
Eur Arch Otorhinolaryngol. 2006 Jul;263(7):627-31. doi: 10.1007/s00405-006-0035-9. Epub 2006 May 3.
Haemangiomas involving the internal auditory meatus (IAM) are rare and can mimic other frequent lesions of the IAM such as schwannomas by their clinical and imaging aspects. The case of a patient with an atypical IAM haemangioma fluctuating in size is reported to highlight this diagnostic possibility. A 36-year-old female presented with a sudden and recurrent left sensorineural hearing loss (SNHL). Three consecutive MRIs were performed in a 10-month period of preoperative observation. They showed a fluctuation of the tumour signal and size. The surgical removal was performed via a translabyrinthine approach. Pathological findings were consistent with the diagnosis of a heamangioma. MRI and CT findings suggested the diagnosis of IAM heamangioma, but the rapid variation in size and signal was misleading. This phenomenon may be due to haemorrhage or oedema, and can be accompanied by a deterioration of the hearing function. Early surgical resection is the treatment of choice and allows to confirm the diagnosis.
累及内耳道(IAM)的血管瘤较为罕见,在临床和影像学表现上可类似IAM的其他常见病变,如神经鞘瘤。本文报告一例大小波动的非典型IAM血管瘤患者,以突出这种诊断可能性。一名36岁女性突发复发性左侧感音神经性听力损失(SNHL)。在术前观察的10个月期间连续进行了三次磁共振成像(MRI)检查。结果显示肿瘤信号和大小有波动。通过经迷路入路进行手术切除。病理结果与血管瘤的诊断一致。MRI和计算机断层扫描(CT)结果提示IAM血管瘤的诊断,但大小和信号的快速变化具有误导性。这种现象可能是由于出血或水肿所致,且可伴有听力功能恶化。早期手术切除是首选治疗方法,可确诊。