Bulycheva I V, Kuz'min I V, Noblz E, Zabazniĭ N P
Arkh Patol. 2006 Mar-Apr;68(2):46-9.
Gangliocytic paraganglioma in a female of 64 years of age with stones in the gall bladder, atrophic liver cirrhosis and gastro-intestinal polyposis is described in the Russian literature for the first time. Polyps of the rectum and sygmoid were removed within 15 years. The same pathology was described by other authors. It is possible that the occurrence of paraganglioma and polyps was of genetical nature. The tumor was detected at gastroduodenoscopy. Biopsy diagnosis varied from polymorphocell liposarcoma and malignant fibrous histiocytoma. Endoscopic tumor electroexcision was complicated by intestinal bleeding that followed by an urgent laparatomy, duodenotomy and suture of the bleeding vessel in the duodenal wall. Bleeding zone in the duodenum was 3 cm from papilla Vateri. Analysis of difficulties in clinical and morphological differential diagnosis is performed.
俄罗斯文献首次描述了一名64岁女性患有神经节细胞性副神经节瘤,同时伴有胆囊结石、萎缩性肝硬化和胃肠道息肉病。在15年内切除了直肠和乙状结肠的息肉。其他作者也描述过相同的病理情况。神经节细胞性副神经节瘤和息肉的发生可能具有遗传性质。该肿瘤在胃十二指肠镜检查时被发现。活检诊断结果不一,包括多形细胞脂肪肉瘤和恶性纤维组织细胞瘤。内镜下肿瘤电切除术并发肠道出血,随后紧急进行剖腹手术、十二指肠切开术并缝合十二指肠壁出血血管。十二指肠出血部位距离 Vater乳头3厘米。对临床和形态学鉴别诊断中的困难进行了分析。