Haddad Wafa, Lahidheb Dhafer, Salah Othman, Rahal Nejib, Barakett Nadia, Smiri Zahreddine, Hajlaoui Nadhem, Mhenni Hédi, Haouala Habib
Service de Cardiologie, Hôpital Militaire de Tunis.
Tunis Med. 2006 Mar;84(3):195-7.
Cor triatrium sinister is a rare congenital disease (0,1% of cases of congenital heart disease). Cor triatrium is recognized by the finding of an abnormal fibromuscular membrane that subdivise the left atrium into posterosuperior and anteroinferor chambers. This anomaly creates an obstacle to the venous pulmonary flow. Depending on the severity of obstruction, cor triatrium may be symptomatic in childhood but it can be symtom free even in adulthood. Diagnosis of this abnormality has been easy supported by transthoracic and transoesophageal echocardiography.Treatment is easy to perform and consists in surgical defenitive correction in symptomatic patients. We report a case of a 31-year-old man in whom a non obstructive cor triatrium was discovered while evaluation for an atrial fibrillation secondary to a hyperthyroidism. According to this rare case we try to evaluate the severity and the outcome of this disease relating the literature data.
左房三房心是一种罕见的先天性疾病(占先天性心脏病病例的0.1%)。三房心通过发现异常的纤维肌性膜将左心房分为后上腔和前下腔而得以确诊。这种异常对肺静脉血流造成障碍。根据梗阻的严重程度,三房心在儿童期可能有症状,但即使在成年期也可能无症状。经胸和经食管超声心动图很容易支持这种异常的诊断。治疗易于实施,对于有症状的患者采用手术确定性矫正。我们报告一例31岁男性,在评估继发于甲状腺功能亢进的房颤时发现非梗阻性三房心。根据这一罕见病例,我们结合文献数据试图评估这种疾病的严重程度和预后。