一种罕见的以腹部肿块为表现的孤立性肠系膜卡斯尔曼病（孤立性肠系膜卡斯尔曼病）。

A rare form of isolated mesenteric Castleman's disease presenting as an abdominal mass (isolated mesenteric Castleman's disease).

作者信息

Papaziogas Basilios, Chatzimavroudis Grigoris, Koutelidakis Ioannis, Grigoriou Marios, Atmatzidis Konstantinos

机构信息

2nd Surgical Clinic, Aristotle University of Thessaloniki, G. Gennimatas Hospital, Thessaloniki, Greece.

出版信息

J Gastrointestin Liver Dis. 2006 Jun;15(2):171-4.

PMID:16802013

Abstract

Castleman's disease is a rare disorder characterized by proliferation of the lymphoid tissue. The most frequent location of the disease is the mediastinum. The location of the disease in the mesentery is rare and it is usually associated with the generalized form of the disease. We report a case of a 22-year old woman with isolated mesenteric Castleman's disease of the lymphoid variant, which presented as a palpable abdominal mass. The final diagnosis was reached after exploratory laparotomy and resection of the tumor. The described case is the first reported case of Castleman's disease of the lymphoid subtype, located in the mesentery.

摘要

卡斯特尔曼病是一种罕见的疾病，其特征为淋巴组织增生。该疾病最常见的发病部位是纵隔。肠系膜部位发病罕见，通常与疾病的全身型相关。我们报告一例22岁女性，患有孤立性肠系膜淋巴型卡斯特尔曼病，表现为可触及的腹部肿块。经剖腹探查及肿瘤切除后得出最终诊断。所描述的病例是首例报道的位于肠系膜的淋巴亚型卡斯特尔曼病。