Anand Pradeep S, Roshna T
Sri Sankara Dental College, Varkala, Kerala State, India.
J Contemp Dent Pract. 2006 Jul 1;7(3):92-8.
Klippel-Trenaunay Syndrome is a rare congenital malformation that may include port-wine stain, soft tissue and bony hypertrophy, and venous malformations and lymphatic abnormalities. Although it usually involves the limbs, it may also rarely involve the head, neck, and orofacial regions. Despite its rarity, Klippel-Trenaunay Syndrome should be considered in the differential diagnosis of gingival enlargement. The condition can be easily recognized clinically, but further investigations including imaging studies have to be carried out in order to better understand the nature of the lesion. This report describes a case of gingival enlargement in Klippel-Trenaunay Syndrome in a 16-year-old female patient. The diagnosis of the condition was made based on the patient history, clinical and radiographic examination, computed tomography (CT), and angiogram.
克-特综合征是一种罕见的先天性畸形,可能包括葡萄酒色斑、软组织和骨肥大,以及静脉畸形和淋巴异常。虽然它通常累及四肢,但也很少累及头、颈和口面部区域。尽管罕见,但在牙龈肿大的鉴别诊断中应考虑克-特综合征。该病症在临床上易于识别,但为了更好地了解病变性质,必须进行包括影像学检查在内的进一步检查。本报告描述了一名16岁女性克-特综合征患者牙龈肿大的病例。该病症的诊断基于患者病史、临床和影像学检查、计算机断层扫描(CT)和血管造影。