Costa J, Ruivo J, Miguéns J, Pimentel J
Laboratory of Neuropathology, Department of Neurology, Santa Maria Hospital, Institute of Molecular Medicine, Lisbon School of Medicine, Lisboa, Portugal.
Acta Neurochir (Wien). 2006 Sep;148(9):977-80. doi: 10.1007/s00701-006-0807-4. Epub 2006 Jul 21.
Gangliogliomas are glioneuronal tumours of the young, and occur more frequently supratentorially. Among those uncommon cases in the spinal cord, the conus medullaris is an extremely rare site. We reviewed the literature of such cases and report another case of a ganglioglioma of the conus in a 13-year-old boy with an insidious sensory sensitive and motor deficit of the right lower limb. Subtotal resection was accomplished with no recurrence after two years of follow-up. As for the supratentorial locations, the extent of surgical resection is the main prognostic factor for gangliogliomas of the spinal cord, and they should be considered in the differential diagnosis of intramedullar neoplasm.
神经节胶质瘤是一种好发于年轻人的神经胶质神经元肿瘤,多发生于幕上。在脊髓的罕见病例中,圆锥是极其罕见的发病部位。我们回顾了此类病例的文献,并报告了另一例13岁男孩圆锥神经节胶质瘤病例,该男孩右下肢隐匿性感觉敏感和运动功能障碍。行次全切除,随访两年无复发。至于幕上部位,手术切除范围是脊髓神经节胶质瘤的主要预后因素,在髓内肿瘤的鉴别诊断中应考虑到它们。