Hanzer M, Riccabona M, Kerbl R
Abteilung für Allgemeine Pädiatrie, Universitätsklinik für Kinder- und Jugendheilkunde Graz, Osterreich.
Klin Padiatr. 2007 Sep-Oct;219(5):292-5. doi: 10.1055/s-2006-933539. Epub 2006 Jul 24.
Malformations of the mullerian-duct-system occur with an incidence of about 0.001-0.005% of the population, and they are frequently associated with unilateral agenesis of the kidney.
A 12-year-old girl presented to our emergency department with cyclic abdominal pain which increased with each of her menses. Ultrasound investigation showed a uterus duplex with obstructed hemivagina and hematometrocolpos as well as an ipsilateral absence of the kidney. Additionally, a cystic expansion in the small pelvis was detected which required further investigations (MRT and MR-angiography) to establish the diagnosis of a hematosalpinx. Excision of the vaginal septum resulted in drainage of the hemato-metrocolpos and the hematosalpinx.
Unilateral hematometrocolpos should be considered as an important differential diagnosis in female adolescents with relapsing lower abdominal pain, even if normal menstruation occurs.
苗勒管系统畸形的发生率约为人口的0.001 - 0.005%,且常与单侧肾发育不全相关。
一名12岁女孩因周期性腹痛前来我院急诊科就诊,每次月经时腹痛加剧。超声检查显示双子宫伴半阴道梗阻及阴道积血、子宫积血,同侧肾脏缺如。此外,在小骨盆内检测到一个囊性扩张,需要进一步检查(磁共振成像和磁共振血管造影)以确诊输卵管积血。切除阴道隔后,阴道积血和输卵管积血得以引流。
即使月经正常,单侧阴道积血也应被视为女性青少年复发性下腹痛的重要鉴别诊断。