与多囊肾相关的丹迪-沃克畸形：重新审视戈德斯顿综合征。
Dandy-Walker malformation associated with polycystic kidneys: Goldston syndrome revisited.
作者信息
Menon Ram K, Nadkarni Trimurti D, Desai Ketan I, Goel Atul
机构信息
Department of Neurosurgery, King Edward Memorial Hospital, Seth G S Medical College, Parel, Mumbai, India.
出版信息
J Clin Neurosci. 2006 Oct;13(8):875-7. doi: 10.1016/j.jocn.2005.09.012. Epub 2006 Aug 23.
A 32-year-old woman was diagnosed with chronic bilateral frontoparietal and interhemispheric subdural haematomas (SDH). Abdominal ultrasonography revealed chronic renal failure due to bilateral large cystic kidneys. Brain MRI demonstrated Dandy-Walker malformation associated with hypoplastic vermis, in addition to the chronic subdural haematomas. This association of polycystic kidneys with Dandy-Walker malformation has been referred to as Goldston or cerebrorenal syndrome. The case is rare and is the first to be reported in an adult patient. The relevant literature is reviewed.
一名32岁女性被诊断为慢性双侧额顶叶及大脑半球间硬膜下血肿（SDH）。腹部超声检查显示双侧大囊性肾导致慢性肾衰竭。脑部磁共振成像（MRI）显示除慢性硬膜下血肿外，还存在与小脑蚓部发育不全相关的Dandy-Walker畸形。多囊肾与Dandy-Walker畸形的这种关联被称为戈德斯顿或脑肾综合征。该病例罕见，是首例在成年患者中报道的。对相关文献进行了综述。
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