先天性感音神经性听力损失中的内耳道狭窄
Internal auditory canal stenosis in congenital sensorineural hearing loss.
作者信息
Sakina M S, Goh B S, Abdullah A, Zulfiqar M A, Saim L
机构信息
Department of Otorhinolaryngology, Faculty of Medicine, Universiti Kebangsaan Malaysia, Jalan Yaacob Latif, Bandar Tun Razak, 56000 Cheras, Kuala Lumpur, Malaysia.
出版信息
Int J Pediatr Otorhinolaryngol. 2006 Dec;70(12):2093-7. doi: 10.1016/j.ijporl.2006.08.001. Epub 2006 Sep 25.
OBJECTIVE
Sensorineural hearing loss (SNHL) due to internal auditory canal (IAC) stenosis with hypoplasia of the cochleovestibular nerve is a rare disorder. The diagnosis of the IAC stenosis requires both high resolution computed tomography scan (HRCT) and magnetic resonance imaging (MRI).
METHODS
A retrospective review over 6 years in an academic tertiary referral center was performed.
RESULTS
Six patients with congenital SNHL were diagnosed with congenital IAC stenosis. Four had unilateral and two had bilateral IAC stenosis after imaging. MRI showed hypoplastic vestibulocochlear nerve in all cases.
CONCLUSIONS
This paper highlights the importance of imaging in diagnosing IAC stenosis and detecting the presence of cochleovestibular nerve in cases of congenital SNHL.
目的
因内耳道（IAC）狭窄合并耳蜗前庭神经发育不全导致的感音神经性听力损失（SNHL）是一种罕见疾病。IAC狭窄的诊断需要高分辨率计算机断层扫描（HRCT）和磁共振成像（MRI）两者。
方法
在一家学术性三级转诊中心进行了为期6年的回顾性研究。
结果
6例先天性SNHL患者被诊断为先天性IAC狭窄。影像学检查后，4例为单侧IAC狭窄，2例为双侧IAC狭窄。MRI显示所有病例的前庭蜗神经发育不全。
结论
本文强调了影像学在诊断IAC狭窄以及检测先天性SNHL病例中耳蜗前庭神经存在情况方面的重要性。
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