Duka Tetyana, Rusnak Milan, Drolet Robert E, Duka Valeriy, Wersinger Christophe, Goudreau John L, Sidhu Anita
Department of Biochemistry, Molecular and Cellular Biology, Georgetown University, Washington, DC, USA.
FASEB J. 2006 Nov;20(13):2302-12. doi: 10.1096/fj.06-6092com.
Many neurodegenerative diseases associated with functional Tau dysregulation, including Alzheimer's disease (AD) and other tauopathies, also show alpha-synuclein (alpha-Syn) pathology, a protein associated with Parkinson's disease (PD) pathology. Here we show that treatment of primary mesencephalic neurons (48 h) or subchronic treatment of wild-type (WT) mice with the Parkinsonism-inducing neurotoxin MPP+/MPTP, results in selective dose-dependent hyperphosphorylation of Tau at Ser396/404 (PHF-1-reactive Tau, p-Tau), with no changes in pSer202 but with nonspecific increases in pSer262 levels. The presence of alpha-Syn was absolutely mandatory to observe MPP+/MPTP-induced increases in p-Tau levels, since no alterations in p-Tau were seen in transfected cells not expressing alpha-Syn or in alpha-Syn-/- mice. MPP+/MPTP also induced a significant accumulation of alpha-Syn in both mesencephalic neurons and in WT mice striatum. MPTP/MPP+ lead to differential alterations in p-Tau and alpha-Syn levels in a cytoskeleton-bound, vs. a soluble, cytoskeleton-free fraction, inducing their coimmunoprecipitation in the cytoskeleton-free fraction and neuronal soma. Subchronic MPTP exposure increased sarkosyl-insoluble p-Tau in striatum of WT but not alpha-Syn-/- mice. These studies describe a novel mechanism for MPTP neurotoxicity, namely a MPTP-inducible, strictly alpha-Syn-dependent, increased formation of PHF-1-reactive Tau, suggesting convergent overlapping pathways in the genesis of clinically divergent diseases such as AD and PD.
许多与功能性Tau蛋白失调相关的神经退行性疾病,包括阿尔茨海默病(AD)和其他tau蛋白病,也表现出α-突触核蛋白(α-Syn)病变,这是一种与帕金森病(PD)病变相关的蛋白质。在此我们表明,用诱导帕金森综合征的神经毒素MPP⁺/MPTP处理原代中脑神经元(48小时)或对野生型(WT)小鼠进行亚慢性处理,会导致Tau蛋白在Ser396/404位点选择性地剂量依赖性过度磷酸化(PHF-1反应性Tau,p-Tau),pSer202无变化,但pSer262水平非特异性升高。α-Syn的存在对于观察MPP⁺/MPTP诱导的p-Tau水平升高绝对必要,因为在未表达α-Syn的转染细胞或α-Syn基因敲除小鼠中未观察到p-Tau的改变。MPP⁺/MPTP还诱导中脑神经元和WT小鼠纹状体中α-Syn的显著积累。MPTP/MPP⁺导致细胞骨架结合部分与可溶性、无细胞骨架部分中p-Tau和α-Syn水平的差异改变,在无细胞骨架部分和神经元胞体中诱导它们的共免疫沉淀。亚慢性MPTP暴露增加了WT小鼠而非α-Syn基因敲除小鼠纹状体中不溶性p-Tau。这些研究描述了MPTP神经毒性的一种新机制,即MPTP诱导的、严格依赖α-Syn的、PHF-1反应性Tau形成增加,提示在AD和PD等临床不同疾病的发生中存在趋同的重叠途径。