Song Zong-ming, Sheng Yan-juan, Chen Qing-shan, Xue An-quan, Lin Bing, Li Ying-zi, Shen Li-jun
Department of Retina, Eye Hospital, Wenzhou Medical College, Wenzhou 325003, China.
Zhonghua Yan Ke Za Zhi. 2006 Aug;42(8):717-23.
To study the clinical manifestations of acute zonal occult outer retinopathy (AZOOR) and to differentiate it from other retinal diseases.
Six patients diagnosed AZOOR had complete eye examinations including fundus photography, fundus fluorescein angiography (FFA), electroretinography (ERG), visual evoked potentials and visual field examination. Medical consultation and neurological consultation were performed in those patients. All patients were followed up and the data were collected for analysis, discussion, diagnosis and differential diagnosis.
Six patients (five female and one male) aged 26 - 42 years (mean 35 years) with AZOOR were followed up for 4 - 18 months [mean (7.5 +/- 3.2) months]. All of them were affected bilaterally and their visual acuity were slightly reduced except one eye was CF/40 cm. Half of them had photopsia. At least one eye of each patient had visual field defect or decreased sensitivity in local area or blind-spot enlargement. Biomicroscopic examination revealed vitreous cells in 10/12 eyes and anterior chamber inflammatory cells and keratic precipitate in 4/12 eyes. Minimal (10/12 eyes) or no (2/12 eyes) fundus changes were found in their initial examination. Funduscopic examination revealed yellow-white dots (4/12 eyes) and gray dots (6/12 eyes) at the posterior pole of deep retina or retinal pigment epithelium-Bruch membrane-choroid capillary complex layer. FFA showed depigmentation (2/12 eyes) or hyperfluorescein spots (10/12 eyes) that identical to the retinal lesions. In the follow-up examination, the visual acuity was reduced in one eye and visual field defect enlarged in both eyes of one patient; the number of retinal dots increased in one eye, decreased in one eye and extinguished in one eye. ERG or mERG revealed abnormal in all of their eyes with no changes in their follow-up examination. All of the initial diagnoses of six patients were not consistent with final diagnosis.
AZOOR is a rare eye disease, usually occurs in young females, with the characteristics of photopsia, visual field defects, abnormal ERG and slight changes in the fundus. The differential diagnosis of this disease is relatively complicate and is easily to be misdiagnosed.
研究急性区域性隐匿性外层视网膜病变(AZOOR)的临床表现,并将其与其他视网膜疾病相鉴别。
6例诊断为AZOOR的患者接受了全面的眼科检查,包括眼底照相、眼底荧光血管造影(FFA)、视网膜电图(ERG)、视觉诱发电位和视野检查。对这些患者进行了内科会诊和神经科会诊。所有患者均进行随访,并收集数据进行分析、讨论、诊断和鉴别诊断。
6例年龄在26 - 42岁(平均35岁)的AZOOR患者(5例女性,1例男性)随访了4 - 18个月[平均(7.5±3.2)个月]。所有患者均双眼受累,除1眼视力为CF/40 cm外,其余患者视力均略有下降。其中半数患者有闪光感。每位患者至少1眼有视野缺损或局部敏感度下降或盲点扩大。生物显微镜检查显示,12眼中10眼有玻璃体细胞,12眼中4眼前房有炎性细胞和角膜后沉着物。初诊时眼底改变轻微(12眼中10眼)或无改变(12眼中2眼)。眼底检查发现,在视网膜深层或视网膜色素上皮- Bruch膜-脉络膜毛细血管复合体层的后极部有黄白色斑点(12眼中4眼)和灰色斑点(~眼中6眼)。FFA显示与视网膜病变一致的色素脱失(12眼中2眼)或高荧光斑点(12眼中10眼)。在随访检查中,1例患者1眼视力下降,双眼视野缺损扩大;1眼视网膜斑点数量增加,1眼减少,1眼消失。ERG或多焦视网膜电图(mERG)显示所有患者双眼均异常,随访检查无变化。6例患者的初诊均与最终诊断不一致。
AZOOR是一种罕见的眼病,通常发生于年轻女性,具有闪光感、视野缺损、ERG异常及眼底轻微改变等特点。本病的鉴别诊断相对复杂,容易误诊。