Le Coz P, Mikol J, Ferrand J, Woimant F, Masters C, Beyreuther K, Haguenau M, Cophignon J, Pepin B
Department of Neurology, Lariboisiere Hospital, Paris VII University, France.
Neuropathol Appl Neurobiol. 1991 Apr;17(2):149-55. doi: 10.1111/j.1365-2990.1991.tb00706.x.
A woman, who presented with clinical and radiological signs of a right temporal mass suggestive of a brain tumour, was found to have granulomatous angiitis associated with cerebral amyloid angiopathy; the diagnosis was confirmed by biopsy. She is still well 13 years after excision of the lesion. The association of granulomatous angiitis and cerebral amyloid angiopathy constitutes a peculiar variety of central nervous system micro-angiopathy. Only a few similar cases have been described.
一名女性患者,临床表现及影像学检查显示右侧颞叶有占位性病变,提示脑肿瘤,经检查发现患有与脑淀粉样血管病相关的肉芽肿性血管炎;活检确诊了该诊断。病变切除13年后,她仍状况良好。肉芽肿性血管炎与脑淀粉样血管病的关联构成了一种特殊类型的中枢神经系统微血管病。仅有少数类似病例被报道过。