Roll M F, Kneppo C, Roth H, Bettendorf M, Waag K-L, Holland-Cunz S
Department of Paediatric Surgery, University Hospital of Heidelberg, Im Neuenheimer Feld 110, 69120 Heidelberg, Germany.
Eur J Pediatr Surg. 2006 Oct;16(5):329-33. doi: 10.1055/s-2006-924602.
The study objective is to evaluate the results of our surgical technique for children with congenital adrenal hyperplasia and ambiguous genitalia at the University Hospital of Heidelberg, Department of Paediatric Surgery. The records of 19 patients with congenital adrenal hyperplasia treated between 1972 and 2004 were reviewed with respect to age at surgery, operative procedures and outcome. We describe the recession clitoroplasty technique currently used in our hospital and highlight the importance of short and long-term follow-up results with respect to appearance, position and size of the clitoris and quality of the vagina. One-stage recession clitoroplasty and vaginoplasty gives very satisfactory cosmetic and functional results, with few complications and a reduced need for secondary surgical interventions. The results of this study support the assumption that total correction can be achieved through a single-stage operation, performed in infancy.
本研究的目的是评估德国海德堡大学医院小儿外科针对先天性肾上腺皮质增生症及生殖器模糊的患儿所采用的手术技术的效果。回顾了1972年至2004年间接受治疗的19例先天性肾上腺皮质增生症患者的记录,内容涉及手术年龄、手术操作及结果。我们描述了目前我院所采用的退缩式阴蒂成形术技术,并强调了对阴蒂的外观、位置和大小以及阴道质量进行短期和长期随访结果的重要性。一期退缩式阴蒂成形术和阴道成形术可带来非常令人满意的美容和功能效果,并发症少,二次手术干预需求降低。本研究结果支持这样一种假设,即通过在婴儿期进行的单阶段手术可实现完全矫正。