穆尼耶-库恩综合征

Mounier-Kuhn syndrome.

作者信息

Fortuna Fabrício Piccoli, Irion Klaus, Wink Cesare, Boemo Jorge Luis

机构信息

Pulmonology Department, Hospital Geral de Caxias do Sul, Caxias do Sul, RS, Brasil.

出版信息

J Bras Pneumol. 2006 Mar-Apr;32(2):180-3. doi: 10.1590/s1806-37132006000200015.

DOI:10.1590/s1806-37132006000200015

PMID:17273589

Abstract

Mounier-Kuhn syndrome, or tracheobronchomegaly, is a rare clinical entity characterized by abnormal dilation of the trachea and main bronchi. The diagnosis can usually be made by measuring the tracheal diameter. We report the case of a 40-year-old black man with refractory lower respiratory tract infection. Tracheobronchomegaly was confirmed through computed tomography.

摘要

穆尼耶 - 库恩综合征，即气管支气管巨大症，是一种罕见的临床病症，其特征为气管和主支气管异常扩张。诊断通常可通过测量气管直径来进行。我们报告一例40岁黑人男性难治性下呼吸道感染病例。通过计算机断层扫描确诊为气管支气管巨大症。