Mert M, Gunay L
Department of Cardiovascular Surgery, Institute of Cardiology, Istanbul University, Istanbul, Turkey.
Acta Chir Belg. 2006 Nov-Dec;106(6):739-40. doi: 10.1080/00015458.2006.11679999.
Morgagni hernia is a rare diaphragmatic hernia occurring secondary to potential anterior medial defects in the diaphragm. The association of the defect with congenital cardiac pathologies and Down syndrome has already been reported. The defect is repaired usually by transabdominal or transthoracic approaches. Transsternal repair of the hernia is preferred in patients undergoing concomitant open heart surgery.
An eight-month old child with Down syndrome and congenital hypothyroidism underwent concomitant repair of Morgagni hernia and closure of his ventricular septal defect under cardiopulmonary bypass. The hernia was repaired by the sternotomy approach, without opening the hernia content, before the correction of the cardiac pathology.
As Morgagni hernia can accompany some congenital cardiac anomalies, cardiac surgeons should be familiar with the transsternal approach to the defect which is as effective as other surgical approaches.
莫尔加尼疝是一种罕见的膈疝，继发于膈肌潜在的前内侧缺损。该缺损与先天性心脏疾病和唐氏综合征的关联已有报道。通常通过经腹或经胸入路修复该缺损。对于同时接受心脏直视手术的患者，经胸骨修复疝更为可取。
一名患有唐氏综合征和先天性甲状腺功能减退症的8个月大儿童在体外循环下同时进行了莫尔加尼疝修补术和室间隔缺损修补术。在纠正心脏病变之前，通过胸骨切开术入路修复疝，未打开疝内容物。
由于莫尔加尼疝可伴有一些先天性心脏异常，心脏外科医生应熟悉经胸骨入路修复该缺损，其效果与其他手术入路相同。
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