Jho David H, Jho Diana J, Chejfec Gregorio, Ahn Maria, Ong Evan S, Espat N Joseph
Department of Surgery, University of Illinois, Chicago, Illinois, USA.
Am Surg. 2007 May;73(5):508-10.
A distinctive case of primary biliary lymphoma occurring in the cystic duct causing extrinsic compression of the porta hepatis in a 48-year-old woman is presented. Imaging studies revealed stricture of the common hepatic duct with a 2.5-cm nonhomogeneous mass at the porta hepatis, mimicking a Klatskin tumor. Exploratory laparotomy revealed a mass in the gallbladder neck with extension into the cystic duct akin to Mirizzi's syndrome. A soft, tan-yellow 1.0-cm mass was removed from the cystic duct, and infiltrating atypical lymphocytic nodules were identified with a final diagnosis of an anaplastic variant of diffuse large B-cell lymphoma.
本文报告了一例48岁女性原发性胆管淋巴瘤的独特病例，该肿瘤发生于胆囊管，导致肝门部受到外部压迫。影像学检查显示肝总管狭窄，肝门部有一个2.5厘米的不均匀肿块，类似肝门部胆管癌。剖腹探查发现胆囊颈部有一个肿块，延伸至胆囊管，类似Mirizzi综合征。从胆囊管中切除了一个1.0厘米的软质棕黄色肿块，经鉴定为浸润性非典型淋巴细胞结节，最终诊断为弥漫性大B细胞淋巴瘤的间变性变体。
