Della Pona C, Rocco G, Rizzi A, Robustellini M, Rossi G, Crasti B
E. Morelli Regional Hospital, Division of Thoracic Surgery, Sondalo, Italy.
Eur Respir J. 1991 Oct;4(9):1140-2.
Lung tissue developmental abnormalities are seldom reported. According to the classification of Schneider (1900), which was amended by Boyden (1955), they include pulmonary agenesis, aplasia and hypoplasia. Due to the early onset of symptoms, lung agenesis and aplasia are usually detected soon after birth. Conversely, lung or lobar hypoplasia may remain clinically silent for a long time. A single case of left lower lobe hypoplasia is reported. A recurring and unrelenting septic fever was the presenting symptom, whilst the radiological picture showed a left lower lobe consolidation. On the surgical specimen gross pathology revealed a lobar hypoplasia. At a short-term follow-up (nine months) the patient shows good overall condition, being free from further complications.
肺组织发育异常鲜有报道。根据施奈德(1900年)的分类,并经博伊登(1955年)修订,其包括肺不发育、肺发育不全和肺发育不良。由于症状出现早,肺不发育和肺发育不全通常在出生后不久就被发现。相反,肺或肺叶发育不良在临床上可能长期无症状。本文报告一例左肺下叶发育不良病例。反复持续的败血症热为首发症状,而影像学表现为左肺下叶实变。手术标本的大体病理显示为肺叶发育不良。在短期随访(9个月)中,患者整体状况良好,未出现进一步并发症。