Kukreja Manu, Gupta Ritesh, Julka Anurag, Sharma M C
All India Institute of Medical Sciences, New Delhi, India.
Can J Ophthalmol. 2007 Aug;42(4):624-5.
We report a rare case of a unique variant of schwannoma (neuroblastoma-like schwannoma) in the orbit in a 16-year-old male who presented with proptosis and decreased vision.
Schwannoma with giant rosettes and hyperchromatic small cells was previously designated a neuroblastoma-like schwannoma by Goldblum et al. (Am J Surg Pathol 1994;18[3]:266-73). In the past, 9 cases of this variant of schwannoma have been reported as a painless subcutaneous nodule in various parts of the body, but none has been reported in the orbit so far. This entity must be distinguished from neuroblastoma, neuroectodermal tumor, and malignant change in schwannoma.
我们报告了一例罕见病例，一名16岁男性眼眶内出现神经鞘瘤的一种独特变体（神经母细胞瘤样神经鞘瘤），表现为眼球突出和视力下降。
带有巨大玫瑰花结和深染小细胞的神经鞘瘤先前被戈德布卢姆等人（《美国外科病理学杂志》1994年；18[3]：266 - 73）命名为神经母细胞瘤样神经鞘瘤。过去，已有9例这种神经鞘瘤变体的病例报告为身体各部位的无痛性皮下结节，但迄今为止尚无眼眶内病例的报告。该实体必须与神经母细胞瘤、神经外胚层肿瘤以及神经鞘瘤的恶性变相鉴别。
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