[The use of Doty's extended aortoplasty in binovular twins with congenital supravalvular aortic stenosis].

Binovular twins with congenital supravalvular aortic stenosis underwent Doty's extended aortoplasty. Neither twins displayed signs of Williams syndrome. Peak systolic pressure gradients of 65 and 70 mmHg, respectively, were measured across the stenotic portion at the ascending aortae. After surgery, the pressure gradients were reduced to 15 and 20 mmHg, respectively, at the aortic valves. No new aortic regurgitation was observed postoperatively. It is important that the ascending aorta, including the stenotic part, is symmetrically incised into the noncoronary and the right coronary sinus of Valsalva. The fibrous ring should be removed as completely as possible. Doty's extended aortoplasty is a safe and effective procedure for supravalvular aortic stenosis.