Curzytek Andrzej, Cioch-Domarska Wioletta, Gutkowski Krzysztof, Błaz Witold, Guz Wiesław, Lubas Wojciech
Oddział Chorób Wewnetrznych z Pododdziałem Intensywnej Opieki Kardiologicznej Szpitala MSWiA, ul. Krakowska 16, 35-111 Rzeszów, Poland.
Kardiol Pol. 2007 Aug;65(8):972-6.
Congenitally corrected transposition of the great arteries (CCTGA) is a rare cardiac malformation. This anomaly is characterised by atrioventricular as well as ventriculoarterial discordance. Isolated CCTGA may cause no symptoms until adult life. Most CCTGA cases with concomitant cardiac abnormalities are symptomatic and are therefore usually diagnosed in childhood. In the majority of patients, congestive heart failure secondary to right ventricular dysfunction occurring by the fifth or sixth decade enables diagnosis. We present an oligosymptomatic 55-year-old woman with corrected transposition of the great arteries and coexisting stenosis of pulmonary trunk valve and ventricular septum defect.
先天性矫正型大动脉转位(CCTGA)是一种罕见的心脏畸形。这种异常的特征是房室以及心室动脉不一致。孤立性CCTGA在成年前可能不引起症状。大多数伴有心脏异常的CCTGA病例有症状,因此通常在儿童期被诊断出来。在大多数患者中,由于右心室功能障碍在五六十岁时继发的充血性心力衰竭有助于诊断。我们报告一例55岁症状轻微的女性患者,患有矫正型大动脉转位,并存肺动脉干瓣狭窄和室间隔缺损。