Shin Shou-Ting, Yang Yao-Hsu, Chiang Bor-Luen
Department of Pediatrics, Far Eastern Memorial Hospital, Taipei, Taiwan.
Acta Paediatr Taiwan. 2007 May-Jun;48(3):149-51.
Kimura's disease (KD) is a rare, chronic inflammatory disease, and the etiology is not yet to be determined. The disease is usually found in young Asian men but rarely in Western population. Here, we report an 8-year-old boy with the initial presentation of right upper eyelid swelling. Laboratory tests disclosed peripheral eosinophilia and elevated IgE level. KD with lacrimal gland involvement was diagnosed. Surgical excision was performed several times and steroid was also used, however the disease recurred. Thereafter, steroid, cyclosporine-A and azathioprine were prescribed. The tumor mass resolved and the laboratory data returned to normal level.
木村病(KD)是一种罕见的慢性炎症性疾病,其病因尚未明确。该疾病通常见于年轻的亚洲男性,在西方人群中则很少见。在此,我们报告一名8岁男孩,最初表现为右上眼睑肿胀。实验室检查显示外周嗜酸性粒细胞增多和IgE水平升高。诊断为累及泪腺的木村病。多次进行手术切除并使用了类固醇,但疾病复发。此后,给予类固醇、环孢素A和硫唑嘌呤治疗。肿瘤肿块消退,实验室数据恢复至正常水平。