Nemec Petr, Rybnickova Sylva, Fabian Pavel, Fojtik Zdenek, Soucek Miroslav
Rheumatology Division, Second Department of Internal Medicine, St. Anne's University Hospital, Masaryk University School of Medicine, Pekarská 53, 65691, Brno, Czech Republic.
Clin Rheumatol. 2008 Mar;27(3):381-4. doi: 10.1007/s10067-007-0736-5. Epub 2007 Oct 11.
Retroperitoneal fibrosis (RPF) is a rare inflammatory disease which is characterized by the development of a fibrous process that surrounds the major vessels and organs located within the retroperitoneum. About two thirds of all cases of RPF are idiopathic and are thought to be immunological in origin. Diagnosis of RPF should be considered in patients with unexplained abdominal and low back pain and retroperitoneal lesions. We present a case report of a 59-year-old white male with idiopathic RPF with history of low back pain and weight loss as only symptoms and treated by tamoxifen, corticosteroids, and insertion of JJ endoureteric catheters due to the obstruction of the upper urinary tract.
腹膜后纤维化(RPF)是一种罕见的炎症性疾病,其特征是在腹膜后形成围绕主要血管和器官的纤维性病变。所有RPF病例中约三分之二为特发性,被认为起源于免疫因素。对于不明原因的腹痛、腰痛和腹膜后病变患者,应考虑RPF的诊断。我们报告一例59岁白人男性特发性RPF病例,其仅以腰痛和体重减轻为症状,因上尿路梗阻接受他莫昔芬、皮质类固醇治疗及置入双J输尿管导管。