Paydar Amir, Ordovas Karen G, Reddy Gautham P
Department of Radiology, University of California San Francisco, Suite M396, Box 0628, San Francisco, CA 94143-0628, USA.
Pediatr Cardiol. 2008 Sep;29(5):1004-5. doi: 10.1007/s00246-007-9151-6. Epub 2007 Nov 28.
Magnetic resonance images (MRI) of a pediatric patient with endomyocardial fibrosis secondary to idiopathic hypereosinophilic syndrome are presented. Previously reported in adults, MRI findings of endomyocardial fibrosis in this case include right ventricular diastolic dysfunction, mild systolic dysfunction and extensive subendocardial delayed contrast enhancement. Right atrial enlargement and organized right ventricular thrombus are also demonstrated.
本文展示了一名患有特发性高嗜酸性粒细胞综合征继发心内膜心肌纤维化的儿科患者的磁共振成像(MRI)。此前在成人中已有报道,该病例中心内膜心肌纤维化的MRI表现包括右心室舒张功能障碍、轻度收缩功能障碍以及广泛的心内膜下延迟对比增强。还显示出右心房扩大和有组织的右心室血栓形成。