Comstock Christine H, Lee Wesley, Bronsteen Richard A, Vettraino Ivana, Wechter Daniel
Division of Fetal Imaging, Department of Obstetrics and Gynecology, William Beaumont Hospital, Royal Oak, MI 48073, USA.
J Ultrasound Med. 2008 Jan;27(1):145-8. doi: 10.7863/jum.2008.27.1.145.
The purpose of this series was to evaluate the prenatal sonographic findings and postnatal outcomes in 2 fetuses with mediastinal lymphangiomas.
The fetal images were compared with postnatal imaging and surgical findings.
The 2 fetuses had anechoic mediastinal masses at 25 and 22 weeks, which proved to be lymphangiomas. One, located in the anterior mediastinum, also enveloped the superior vena cava, brachial plexus, phrenic nerve, larynx, and lower parts of the neck vessels and extended into the subcutaneous tissues of the anterior chest wall through an intercostal space. In the second patient, the lymphangioma appeared to be a unilocular cyst, which involved the deep tissues of the neck as well as the posterior and lateral mediastinum. Both required 2 interventions after birth.
Fetal mediastinal lymphangiomas appeared anechoic and sent extensions into the neck in the first case, around the superior vena cava, through the intercostal spaces to the skin, and around the brachial plexus in the second case, and deviated the trachea in both cases. In 1 case, there was also ectasia of the superior vena cava. This ability to entwine around vital structures can make it difficult to determine the extent of involvement on antenatal sonography and to remove lymphangiomas completely, and recurrence is common.
本系列研究旨在评估2例纵隔淋巴管瘤胎儿的产前超声检查结果及产后结局。
将胎儿期图像与产后影像学及手术结果进行对比。
2例胎儿在孕25周和22周时出现纵隔无回声肿块,术后证实为淋巴管瘤。1例位于前纵隔,还包绕上腔静脉、臂丛神经、膈神经、喉以及颈部血管下段,并通过肋间间隙延伸至前胸壁皮下组织。第2例患者的淋巴管瘤表现为单房囊肿,累及颈部深层组织以及后纵隔和侧纵隔。2例患儿出生后均需进行2次干预。
胎儿纵隔淋巴管瘤在第1例中表现为无回声,向颈部延伸,包绕上腔静脉,通过肋间间隙延伸至皮肤,在第2例中包绕臂丛神经,且2例均使气管移位。1例还存在上腔静脉扩张。这种缠绕重要结构的能力使得产前超声难以确定受累范围,也难以完全切除淋巴管瘤,且复发很常见。