de Vries Jan J, Vogten Jan M, de Bruin Peter C, Boerma Djamila, van de Pavoordt Henricus D W M, Hagendoorn Jeroen
Department of General Surgery, St Antonius Hospital, Nieuwegein, The Netherlands.
Lymphat Res Biol. 2007;5(4):269-73. doi: 10.1089/lrb.2007.1010.
Lymphangiomas are benign tumors consisting of lymphatic vasculature that generally occur in the skin and soft tissues. Rarely, lymphangiomas occur in the gastrointestinal tract. Here, we report a case of a 13-year-old girl presenting with an intestinal obstruction. Upon laparotomy, multiple cystic masses in the mesentery causing a volvulus were resected and histologically identified as multiple lymphangiomas, or lymphangiomatosis. Mesenteric lymphangioma is a rare entity, but should be considered as cause of bowel obstruction without other known abdominal disease. As the etiology of lymphangiomas remains elusive, further research is directed at unravelling the mechanistic and molecular factors contributing to this disease.
淋巴管瘤是由淋巴管组成的良性肿瘤,通常发生于皮肤和软组织。淋巴管瘤很少发生在胃肠道。在此,我们报告一例13岁女孩出现肠梗阻的病例。剖腹手术时,切除了肠系膜中导致肠扭转的多个囊性肿物,组织学检查确定为多发淋巴管瘤,即淋巴管瘤病。肠系膜淋巴管瘤是一种罕见的疾病,但在没有其他已知腹部疾病的情况下,应将其视为肠梗阻的病因。由于淋巴管瘤的病因仍不清楚,进一步的研究旨在揭示导致这种疾病的机制和分子因素。