颈内循环纤维肌发育不良：一种不寻常的表现。

Fibromuscular dysplasia of the internal carotid circulation: an unusual presentation.

作者信息

Bhuriya Rohitkumar, Arora Rohit, Khosla Sandeep

机构信息

Department of Medicine, The Chicago Medical School at Rosalind Franklin University, 3333 Green Bay Road, North Chicago, IL 60064, USA.

出版信息

Vasc Med. 2008 Feb;13(1):41-3. doi: 10.1177/1358863X07085530.

DOI:10.1177/1358863X07085530

PMID:18372438

Abstract

Fibromuscular dysplasia (FMD) is an arterial disease of unknown etiology. Most often it affects the renal and internal carotid arteries (ICA), although any artery can be involved. Internal carotid arteries are affected in 25-30% of patients. When carotid arteries are involved, cervical segments C1-C2 are most often affected. FMD of intracranial arteries is rare. FMD has been associated with intracranial aneurysms in 7-50% cases, but FMD associated with a giant (> 2.5 cm) intracranial aneurysm is rare. Extracranial internal carotid aneurysms are uncommon, with only 3% caused by FMD. We report a case of intra and extracranial FMD associated with a giant intracranial aneurysm and an aneurysm of the right extracranial ICA.

摘要

纤维肌发育不良（FMD）是一种病因不明的动脉疾病。它最常累及肾动脉和颈内动脉（ICA），不过任何动脉都可能受累。25%至30%的患者颈内动脉会受到影响。当颈动脉受累时，C1 - C2颈椎节段最常受到影响。颅内动脉的FMD较为罕见。在7%至50%的病例中，FMD与颅内动脉瘤有关，但FMD与巨大（>2.5厘米）颅内动脉瘤相关的情况罕见。颅外颈内动脉瘤并不常见，仅3%由FMD引起。我们报告一例伴有巨大颅内动脉瘤和右侧颅外ICA动脉瘤的颅内及颅外FMD病例。