Boussouga Mostapha, Harket Anas, Bousselmame Nabile, Lazrak Khalid
Orthopaedic surgery department, Mohamed V Military Hospital, Rabat, Morocco.
Acta Orthop Belg. 2008 Feb;74(1):114-7.
Lymphangioleiomyomatosis (LAM) is a rare condition usually occurring in young women of childbearing age. It is characterised by the presence of abnormal smooth muscle cells (LAM cells) in the lungs, lymph nodes, and/or other organs, with a few reports of isolated extrapulmonary cases. We report the case of a 26-yr-old female who presented with a painless shoulder mass. Ultrasonography, computed tomography and magnetic resonance imaging revealed an intermuscular mass with cystic and solid tissue components, measuring 6 cm x 4 cm. The mass was removed surgically after the diagnosis of LAM was made following tru-cut biopsy. This case corresponds to an exceptional localisation of LAM.
淋巴管平滑肌瘤病(LAM)是一种罕见疾病,通常发生在育龄期年轻女性中。其特征是肺部、淋巴结和/或其他器官中存在异常平滑肌细胞(LAM细胞),仅有少数孤立的肺外病例报道。我们报告一例26岁女性,她出现无痛性肩部肿块。超声、计算机断层扫描和磁共振成像显示为肌间肿块,有囊性和实性组织成分,大小为6厘米×4厘米。在经皮穿刺活检确诊为LAM后,该肿块被手术切除。此病例属于LAM的特殊定位。