Lebensburger Jeffrey, Esbenshade Adam, Blakely Martin, Hankins Jane, Wang Winfred
Department of Hematology, St. Jude Children's Research Hospital, Memphis, Tennessee, USA.
Pediatr Blood Cancer. 2008 Aug;51(2):288-90. doi: 10.1002/pbc.21575.
Spontaneous biloma and pneumobilia developed in a patient with sickle cell disease (SCD) who presented with acute abdominal pain, jaundice, and fever. Bilomas are fluid-filled cysts that develop from a bile leak and are located outside of the biliary system. Pneumobilia is characterized by gas within the biliary system due to an abnormal connection between the biliary tree and adjacent organs, particularly the gastrointestinal tract. Although hepatobiliary complications are common in SCD, we report on biloma and pneumobilia in a young patient with this condition.
一名患有镰状细胞病(SCD)的患者出现了自发性胆汁瘤和气肿性胆囊炎,该患者表现为急性腹痛、黄疸和发热。胆汁瘤是由胆汁渗漏形成的充满液体的囊肿,位于胆道系统之外。气肿性胆囊炎的特征是由于胆道树与相邻器官,特别是胃肠道之间的异常连接,导致胆道系统内出现气体。尽管肝胆并发症在SCD中很常见,但我们报告了一名患有这种疾病的年轻患者出现胆汁瘤和气肿性胆囊炎的情况。