Rapsyn羧基末端结构域介导肌肉特异性激酶诱导的肌肉乙酰胆碱受体磷酸化。

Rapsyn carboxyl terminal domains mediate muscle specific kinase-induced phosphorylation of the muscle acetylcholine receptor.

作者信息

Lee Y, Rudell J, Yechikhov S, Taylor R, Swope S, Ferns M

机构信息

Departments of Anesthesiology and Physiology and Membrane Biology, One Shields Avenue, University of California-Davis, Davis, CA 95616, USA.

出版信息

Neuroscience. 2008 Jun 2;153(4):997-1007. doi: 10.1016/j.neuroscience.2008.03.009. Epub 2008 Mar 18.

Abstract

At the developing vertebrate neuromuscular junction, postsynaptic localization of the acetylcholine receptor (AChR) is regulated by agrin signaling via the muscle specific kinase (MuSK) and requires an intracellular scaffolding protein called rapsyn. In addition to its structural role, rapsyn is also necessary for agrin-induced tyrosine phosphorylation of the AChR, which regulates some aspects of receptor localization. Here, we have investigated the molecular mechanism by which rapsyn mediates AChR phosphorylation at the rodent neuromuscular junction. In a heterologous COS cell system, we show that MuSK and rapsyn induced phosphorylation of beta subunit tyrosine 390 (Y390) and delta subunit Y393, as in muscle cells. Mutation of beta Y390 or delta Y393 did not inhibit MuSK/rapsyn-induced phosphorylation of the other subunit in COS cells, and mutation of beta Y390 did not inhibit agrin-induced phosphorylation of the delta subunit in Sol8 muscle cells; thus, their phosphorylation occurs independently, downstream of MuSK activation. In COS cells, we further show that MuSK-induced phosphorylation of the beta subunit was mediated by rapsyn, as MuSK plus rapsyn increased beta Y390 phosphorylation more than rapsyn alone and MuSK alone had no effect. Intriguingly, MuSK also induced tyrosine phosphorylation of rapsyn itself. We then used deletion mutants to map the rapsyn domains responsible for activation of cytoplasmic tyrosine kinases that phosphorylate the AChR subunits. We found that rapsyn C-terminal domains (amino acids 212-412) are both necessary and sufficient for activation of tyrosine kinases and induction of cellular tyrosine phosphorylation. Moreover, deletion of the rapsyn RING domain (365-412) abolished MuSK-induced tyrosine phosphorylation of the AChR beta subunit. Together, these findings suggest that rapsyn facilitates AChR phosphorylation by activating or localizing tyrosine kinases via its C-terminal domains.

摘要

在发育中的脊椎动物神经肌肉接头处,乙酰胆碱受体(AChR)的突触后定位受聚集蛋白信号通过肌肉特异性激酶(MuSK)调控,且需要一种名为rapsyn的细胞内支架蛋白。除了其结构作用外,rapsyn对于聚集蛋白诱导的AChR酪氨酸磷酸化也是必需的,该磷酸化调节受体定位的某些方面。在此,我们研究了rapsyn在啮齿动物神经肌肉接头处介导AChR磷酸化的分子机制。在异源COS细胞系统中,我们发现,与在肌肉细胞中一样,MuSK和rapsyn诱导β亚基酪氨酸390(Y390)和δ亚基Y393磷酸化。β Y390或δ Y393突变并不抑制COS细胞中MuSK/rapsyn诱导的另一亚基磷酸化,且β Y390突变并不抑制Sol8肌肉细胞中聚集蛋白诱导的δ亚基磷酸化;因此,它们的磷酸化是独立发生的,在MuSK激活的下游。在COS细胞中,我们进一步发现,MuSK诱导的β亚基磷酸化由rapsyn介导,因为MuSK加rapsyn比单独的rapsyn更能增加β Y390磷酸化,而单独的MuSK则无作用。有趣的是,MuSK还诱导rapsyn自身的酪氨酸磷酸化。然后,我们使用缺失突变体来确定负责激活磷酸化AChR亚基的细胞质酪氨酸激酶的rapsyn结构域。我们发现,rapsyn C末端结构域(氨基酸212 - 412)对于酪氨酸激酶的激活和细胞酪氨酸磷酸化的诱导既是必需的也是充分的。此外,rapsyn RING结构域(365 - 412)的缺失消除了MuSK诱导的AChRβ亚基酪氨酸磷酸化。总之,这些发现表明rapsyn通过其C末端结构域激活或定位酪氨酸激酶来促进AChR磷酸化。

文献AI研究员

20分钟写一篇综述,助力文献阅读效率提升50倍

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索