Guo Wei, Lasky Joseph L, Chang Chun-Ju, Mosessian Sherly, Lewis Xiaoman, Xiao Yun, Yeh Jennifer E, Chen James Y, Iruela-Arispe M Luisa, Varella-Garcia Marileila, Wu Hong
Department of Molecular and Medical Pharmacology, University of California, Los Angeles, Los Angeles, California 90095, USA.
Nature. 2008 May 22;453(7194):529-33. doi: 10.1038/nature06933. Epub 2008 May 7.
Cancer stem cells, which share many common properties and regulatory machineries with normal stem cells, have recently been proposed to be responsible for tumorigenesis and to contribute to cancer resistance. The main challenges in cancer biology are to identify cancer stem cells and to define the molecular events required for transforming normal cells to cancer stem cells. Here we show that Pten deletion in mouse haematopoietic stem cells leads to a myeloproliferative disorder, followed by acute T-lymphoblastic leukaemia (T-ALL). Self-renewable leukaemia stem cells (LSCs) are enriched in the c-Kit(mid)CD3(+)Lin(-) compartment, where unphosphorylated beta-catenin is significantly increased. Conditional ablation of one allele of the beta-catenin gene substantially decreases the incidence and delays the occurrence of T-ALL caused by Pten loss, indicating that activation of the beta-catenin pathway may contribute to the formation or expansion of the LSC population. Moreover, a recurring chromosomal translocation, T(14;15), results in aberrant overexpression of the c-myc oncogene in c-Kit(mid)CD3(+)Lin(-) LSCs and CD3(+) leukaemic blasts, recapitulating a subset of human T-ALL. No alterations in Notch1 signalling are detected in this model, suggesting that Pten inactivation and c-myc overexpression may substitute functionally for Notch1 abnormalities, leading to T-ALL development. Our study indicates that multiple genetic or molecular alterations contribute cooperatively to LSC transformation.
癌症干细胞与正常干细胞具有许多共同特性和调控机制,最近有人提出它们对肿瘤发生负责并导致癌症耐药。癌症生物学的主要挑战是识别癌症干细胞,并确定将正常细胞转化为癌症干细胞所需的分子事件。在此我们表明,小鼠造血干细胞中Pten基因的缺失会导致骨髓增殖性疾病,随后发展为急性T淋巴细胞白血病(T-ALL)。自我更新的白血病干细胞(LSC)富集于c-Kit(mid)CD3(+)Lin(-)细胞区室,其中未磷酸化的β-连环蛋白显著增加。β-连环蛋白基因一个等位基因的条件性缺失可大幅降低由Pten缺失引起的T-ALL的发病率并延迟其发生,这表明β-连环蛋白信号通路的激活可能有助于LSC群体的形成或扩增。此外,一种反复出现的染色体易位T(14;15)导致c-Kit(mid)CD3(+)Lin(-)LSC和CD3(+)白血病母细胞中c-myc癌基因异常过表达,重现了一部分人类T-ALL的情况。在该模型中未检测到Notch1信号通路的改变,这表明Pten失活和c-myc过表达可能在功能上替代了Notch1异常,从而导致T-ALL的发生。我们的研究表明,多种基因或分子改变协同促成了LSC的转化。