Hosler Gregory A, Liégeois Nanette, Anhalt Grant J, Moresi J Margaret
Department of Dermatology, Johns Hopkins University, Baltimore, MD, USA.
J Cutan Pathol. 2008 Nov;35(11):1063-7. doi: 10.1111/j.1600-0560.2007.00931.x. Epub 2008 Jun 9.
Subcutaneous gamma/delta (gamma/delta) T-cell lymphoma is a rare lymphoma, characterized by its unique immunophenotype and clinical course. It has been shown to behave more aggressively than its counterpart bearing the alpha/beta receptor and has recently been removed from the subcutaneous panniculitis-like T-cell lymphoma category for this very reason. We present a case of a patient with a 15-year running diagnosis of panniculitis. Following these years of indolent behavior, the disease began an aggressive clinical course and she was diagnosed with gamma/delta T-cell lymphoma. Molecular analysis identified a T-cell clone, which through retrospective analysis, was also shown to be present in the patient's original biopsy material. We present this case as a rare example of initial indolent behavior in a lymphoma typically considered very aggressive.
皮下γ/δ(γ/δ)T细胞淋巴瘤是一种罕见的淋巴瘤,其特征在于独特的免疫表型和临床病程。已证明它比具有α/β受体的同类淋巴瘤侵袭性更强,正因为如此,它最近已从皮下脂膜炎样T细胞淋巴瘤类别中移除。我们报告一例有15年脂膜炎诊断史的患者。在经历了这些年的惰性病程后,疾病开始了侵袭性临床病程,她被诊断为γ/δT细胞淋巴瘤。分子分析鉴定出一个T细胞克隆,通过回顾性分析发现该克隆也存在于患者最初的活检材料中。我们将此病例作为一个罕见的例子呈现,即一种通常被认为侵袭性很强的淋巴瘤最初表现为惰性病程。